Pediatric Microtia

What is Pediatric Microtia?

Microtia is when a baby is born with a smaller ear than normal. The ear is usually so abnormally shaped and small that it no longer looks like an ear, and it is occasionally completely absent (anotia). In the majority of children this occurs on only one side, where the other ear is of normal dimensions. There are several grading systems used to describe how severe the microtia is. 

What are the different types of  Pediatric Microtia?

The mildest form of microtia is when the ear appears smaller than usual but still has most of the features that a normal ear has. The most common scenario is one where the cartilage part of the ear is very small and abnormally shaped and the ear lobe is present, but rotated forward and upward giving it an abnormal appearance. In this most common scenario, the ear canal is also absent or very narrowed. When the ear canal is absent it is called aural atresia. If aural atresia is present the child should be evaluated by an Ears, Nose and Throat (ENT) specialist to determine what the effects on hearing are and what if anything should be done to improve hearing.

It is important to note that microtia is most often associated with a process called craniofacial microsomia which is also called hemifacial microsomia. This condition is present when there are abnormally small features present on one or both sides of the face. Craniofacial microsomia is believed to be due to an abnormal circulation of blood to the face during development which leads to decreased growth of the skin, fat and bone of the face and often microtia.

More rare conditions are also associated with microtia. These include Goldenhar syndrome and Treacher Collins syndrome. These patients can have multiple issues in addition to craniofacial microsomia and microtia and should be treated in a special way for these reasons. 

Pediatric Microtia Doctors and Providers